Double-Chambered Right Ventricle (DCRV) And Large Apical Ventricular Septal Defect (VSD)

Double-chambered right ventricle (DCRV) is a form of right ventricular outflow tract obstruction. It typically presents in childhood or adolescence. It is a form of right ventricular (RV) outflow tract obstruction caused by anomalous muscular or fibromuscular bundles that divide the right ventricle into proximal high-pressure and distal low-pressure chambers. Those muscle bundles run between an area located in the ventricular septum, beneath the level of the septal leaflet of the tricuspid valve, and the anterior wall of the RV. However, no uniformity is observed in the position of these anomalous muscle bundles or in the manner in which the RV is divided. Symptoms of double-chambered right ventricle (DCRV) that require therapy are generally an indication for operative repair. The ventricular septal defect is a defect in the ventricular septum which consists of an inferior muscular and superior membranous portion. VSD is usually symptomless at birth and usually manifests a few weeks after birth. During ventricular contraction, or systole, some of the blood from the left ventricle leaks into the right ventricle, passes through the lungs and reenters the left ventricle via the pulmonary veins and left atrium. It can be detected by cardiac auscultation.Treatment is either conservative or surgical. Video by Maged Al Ali MD